Lipid metabolism — Flashcards

_____ deficiency is characterized by an inability to break down medium-sized fatty acids

Vitamin B7 (biotin) is a cofactor for the enzyme _____ (fatty acid synthesis)

Which lysosomal storage disease is characterized by a cherry red spot on the macula and hepatosplenomegaly? _____

In the _____, the HMP shunt provides a source of NADPH for biosynthesis of fatty acids, cholesterol, and steroids

HMG-CoA may be converted to _____ via the enzyme HMG-CoA lyase (ketogenesis)

Bile acids, derived from _____, are released into the intestinal lumen

_____ deficiency is an inherited defect in the transport of long chain fatty acids into the mitochondria

Which enzyme of the fatty acid synthesis pathway utilizes NADPH? _____

Which membrane-bound organelle is involved in the catabolism of very-long-chain fatty acids, branched-chain fatty acids, amino acids, and ethanol? _____

Fatty acyl-carnitine is transported from the intermembrane space into the mitochondrial matrix via the _____ transporter