Rheumatology & Haematology — Flashcards
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~80% of cases are haemophilia _____ caused by genetic factor VIII deficiency
Haemophilias present with _____ commonly affecting the knees, ankles, & elbows; recurrent ecchymoses; and prolonged haemorrhage particularly after surgery/procedures
In haemophilia A, mixing normal plasma with the patient's plasma (mixing study) _____ correct the aPTT
Hint: does/doesn't
Management of beta thalassemia major involves chronic _____, which increases risk for secondary hemochromatosis
Alpha thalassaemia _____ is due to --/-- and is incompatible with life.
What is the management for essential thrombocythaemia? _____ to prevent thrombosis Hydroxyurea to ↓ platelets
Alpha thalassaemia _____ is due to -α/αα and presents asymptomatically
hydroxycarbamide(hydroxyurea) is useful in the treatment of sickle cell disease because it increases ↑ levels of _____ (typically >15%)
Sickle cell disease can cause _____ due to vaso-occlusion in the pulmonary vasculature
What is the most common acute complication/event in sickle cell disease? _____
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