Rheumatology & Haematology — Flashcards

What is the management for essential thrombocythaemia? _____ to prevent thrombosis Hydroxyurea to ↓ platelets

_____ is a haemoglobinopathy due to decreased synthesis of globin chains

Management of beta thalassemia major involves chronic _____, which increases risk for secondary hemochromatosis

What is the most accurate investigation for haemophilia? _____

Which coagulation disorder presents with recurrent haemarthroses, spontaneous / easy bruising, and bleeding after surgery? _____

What is the general management for thalassaemia intermedia or haemoglobin H disease (- -/-α)? _____

Alpha thalassaemia major (haemoglobin Bart's disease) often results in _____ in utero

What is the general management for thalassaemia major? _____

Hint: 2

Thalassaemia is associated with a(n) _____ red cell distribution width (RDW)

Thalassaemia genes are inherited in an _____ fashion.