Amino Acid Metabolism — Flashcards

Argininosuccinate may be broken down into _____ and fumarate via the enzyme argininosuccinase

NH3 is excreted in the urine primarily in the form of _____ (from the liver) and NH4+ (from glutamine breakdown)

Methylmalonyl-CoA may be converted to _____ via the enzyme methylmalonyl-CoA mutase (with vitamin B12 as a cofactor)

_____ may be combined with aspartate to form argininosuccinate via the enzyme argininosuccinate synthetase (requires 1 ATP)

In the liver, amino acids transfer their NH3 group to _____, forming glutamate and -ketoacids

A positive _____ test may help in the diagnosis of cystine kidney stones

The amino acids _____ and arginine are positively charged at body pH (basic)

Fumarylacetoacetate converts to _____ and Acetoacetate with the help of enzyme hydrolase

The treatment for propionic acidemia is a low _____ diet that does not include valine, methionine, isoleucine, or threonine

_____ is synthesized from L-arginine via NO synthase